Publication:
Successful use of sirolimus for refractory atrial ectopic tachycardia in a child with cardiac rhabdomyoma

dc.contributor.authorNinic, Sanja (51864038300)
dc.contributor.authorKalaba, Marija (36094568600)
dc.contributor.authorJovicic, Bosiljka (54417394900)
dc.contributor.authorVukomanovic, Vladislav (55881072000)
dc.contributor.authorPrijic, Sergej (20734985500)
dc.contributor.authorVucetic, Biljana (57947350900)
dc.contributor.authorKravljanac, Ruzica (6506380739)
dc.contributor.authorVujic, Ana (57218797558)
dc.contributor.authorKosutic, Jovan (55928740700)
dc.date.accessioned2025-06-12T17:18:07Z
dc.date.available2025-06-12T17:18:07Z
dc.date.issued2017
dc.description.abstractCardiac rhabdomyomas are common in tuberous sclerosis. We report a child who developed rhabdomyoma related arrhythmia refractory to antiarrhythmic drug therapy. Reversion of the atrial ectopic tachycardia was achieved with mammalian target of rapamycin pathway (mTOR) inhibitor sirolimus. As per our knowledge, this is the first time that sirolimus has been successfully used in this setting. © 2017 Wiley Periodicals, Inc.
dc.identifier.urihttps://doi.org/10.1111/anec.12435
dc.identifier.urihttps://www.scopus.com/inward/record.uri?eid=2-s2.0-85013361062&doi=10.1111%2fanec.12435&partnerID=40&md5=2c87a475a570ae7610975fd81219dec4
dc.identifier.urihttps://remedy.med.bg.ac.rs/handle/123456789/6897
dc.subjectarrhythmia
dc.subjectm-TOR inhibitor
dc.subjectrhabdomyoma
dc.subjectsirolimus
dc.titleSuccessful use of sirolimus for refractory atrial ectopic tachycardia in a child with cardiac rhabdomyoma
dspace.entity.typePublication

Files