Krasic, Stasa (57192096021)Stasa (57192096021)KrasicDizdarevic, Ivan (57216609439)Ivan (57216609439)DizdarevicVranic, Lana (57362200400)Lana (57362200400)VranicNešić, Dejan (26023585700)Dejan (26023585700)NešićVukomanovic, Vladislav (55881072000)Vladislav (55881072000)Vukomanovic2025-07-022025-07-022023https://doi.org/10.3390/jcdd10110460https://www.scopus.com/inward/record.uri?eid=2-s2.0-85178093332&doi=10.3390%2fjcdd10110460&partnerID=40&md5=dc3dde3cff31f9c5594545cc71441ddehttps://remedy.med.bg.ac.rs/handle/123456789/11709Clinical presentation, course, and treatment for patients with isolated right ventricular (RV) hypoplasia (IRVH) depends on the degree of hypoplasia that is present—this is a spectrum from spontaneous maturation to Fontan circulation over time. An 8-month-old infant presented with IRVH; in the patient, a modified Blalock–Taussig (MBTS) shunt was closed percutaneously after spontaneous RV function recovery. A female newborn was diagnosed with differential cyanosis at birth. The echocardiography showed a hypertrophic RV with a small cavity, a right–left shunt on the atrial septal defect, an almost closed ductus arteriosus (DA), and a small tricuspid valve ring (Z-score-2) with mild regurgitation (pressure gradient 30 mmHg). On the 4th day of life, the patient showed deepened cyanosis and hyperlactatemia was registered. The echocardiography examination revealed a closed DA. Right ventriculography performed on the 5th day of life evidenced the presence of a small hypertrabeculated RV. The pressure in the RV increased. A right-side MBTS was created on the 6th day of life. Further echocardiographic findings indicated a gradual development of the RV and a decrease in RV pressure. MBTS occlusion was performed when the patient was 8 months old. Vital parameters were monitored invasively and noninvasively after the balloon occlusion of MBTS. Percutaneous MBTS occlusion was successfully performed using an Amplatzer vascular plug 2 (AVP2). During the follow-up period, the patient was found to have maintained a normal percutaneous oxyhaemoglobin blood saturation. © 2023 by the authors.AVP2isolated right ventricular hypoplasiaMBTSMBTS percutaneous closure